Case Summary:
A 35-year-old healthy female presented with longstanding unilateral visual decline in the left eye. No prior ocular history.
Exam Findings:
VA: 6/6 OD, 6/40 OS
Anterior Segment: Unremarkable OU
Fundus:
OD: Normal
OS: Congested, tortuous vessels with a vasoproliferative-appearing lesion, highly suggestive of racemose hemangioma
FA Findings:
OD: Unremarkable
OS: Rapid filling without leakage, neovascularization, or ischemia
Diagnosis & Plan:
Diagnosis is racemose hemangioma. The patient was referred for CT angiography to assess cerebrovascular involvement.
Racemous hemangioma of the retina (RRH) is a rare congenital retinal arteriovenous malformation characterized by anomalous arteriovenous communications. Thirty percent of patients with RRH have also been found to have Wybrun-Mason syndrome, an arteriovenous malformation in the brain. Therefore, it is important to exclude this pathology with brain MRI.
Credit: Anas Igbariye, MD
Affiliation: Bnai Zion Medical Center
Instagram Account: @iseeoph Instagram Personal Account: @anasigbariye
Caption editing: M. Giray Ersoz, MD, FEBO
Biruni University School of Medicine, Department of Ophthalmology, Istanbul, Turkey
Instagram accounts: @retina.review and @retina.dr.girayersoz